Anusha I¹*, Shobana N², Selvakumar CJ³ and Sadeeshkumar V³

¹Resident, Department of Neurology, Coimbatore Medical College, Tamil Nadu, India
²Professor and HOD, Department of Neurology, Coimbatore Medical College, Tamil Nadu, India
³Assistant Professor, Department of Neurology, Coimbatore Medical College, Tamil Nadu, India

*Corresponding Author: Anusha I, Resident, Department of Neurology, Coimbatore Medical College, Tamil Nadu, India.

Received: September 02, 2025; Published: September 27, 2025

Abstract

Palatal tremors are subdivided into essential (EPT) and symptomatic (SPT) forms according to clinical and etiological features. A subgroup of the SPT form has a syndrome of progressive ataxia and palatal tremor (PAPT). PAPT may be divided into sporadic and familial forms. In sporadic PAPT patients typically have olivary hypertrophy and increases signal intensity on T2-weighted MRI and progressive cerebellar degeneration. Familial form shows marked atrophy of cervical cord and brainstem with corticospinal signs, the hypertrophic olivary appearance on MRI will be absent. Few clinical features and MRI characteristics can help in differentiating familial and sporadic form even when genetic tests are inconclusive.
Here we describe a rare case of Progressive Ataxia with Palatal Tremors(PAPT) with features suggestive of familial form with inconclusive genetic tests.

Keywords: Palatal Tremors; progressive ataxia; olivary hypertrophy

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Citation

Citation: Anusha I., et al. “A Rare Case of Progressive Ataxia with Palatal Tremors".Acta Scientific Neurology 8.10 (2025): 92-96.

Copyright

Copyright: © 2025 Anusha I., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.