Acta Scientific Neurology (ASNE) (ISSN: 2582-1121)

Case Report Volume 7 Issue 1

A Case of Giant Scalp Neurofibroma

Roshan Khaswada1* and Tamang R2

1MCh Neurosurgery, Koshi Hospital, Biratnagar, Nepal
2General Surgery, Koshi Hospital Biratnagar, Nepal

*Corresponding Author: Khaswada, MCh Neurosurgery, Koshi Hospital, Biratnagar, Nepal.

Received: October 10, 2023; Published: January 03, 2024

Abstract

Objective: To report a rare case of giant scalp Neurofibroma in eighteen year male presenting with ulceration of overlying skin with recurrent bleeding.

Case Report: A eighteen year male presented with giant neurofibroma in front temper occipital region with ulceration in occipital region due to pressure sore with difficulty in sleeping in supine position. He had family history of similar lesions in his mother and sister suggestive of hereditary origin. CT head showed calvarial defect in torcular heropili.

Conclusion: Genetic counselling is necessary before getting married and having children because neurofibromatosis is an inherited condition that runs in the autosomal dominant gene family. Decisions regarding indications for and scope of surgery need to be tailored to the tumour extent, location radiologic features, and within the context of the individual patient’s overall health.

Keywords: Giant Neurofibroma; Neurofibromatosis; NF1; Plexiform

References

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  9. Dimitrova V., et al. “A case of neurofibromatosis type 1”. Journal of IMAB 1 (2008): 63-67.
  10. Bekisz O., et al. “Diffuse but unilateral gingival enlargement associated with von Recklinghausen neurofibromatosis: A case report”. Journal of Clinical Periodontology 27 (2000): 361-365.
  11. Gucev Z., et al. “Four generations in a family with neurofibromatosis 1: Precocious puberty and optic nerve tumor (OPT)”. Prilozi 31 (2010): 253-259.
  12. White SC and Pharoh MJ. “Oral radiology principles and interpretation”. 6th edition. Louis: Mosby (2009).

Citation

Citation: Roshan Khaswada and Tamang R. “A Case of Giant Scalp Neurofibroma". Acta Scientific Neurology 7.2 (2024): 03-05.

Copyright

Copyright: © 2024 Roshan Khaswada and Tamang R. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.




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