Acta Scientific Gastrointestinal Disorders (ASGIS)(ISSN: 2582-1091)

Research Article Volume 6 Issue 9

Undifferentiated Embryonal Sarcoma of the Liver. Clinical Features and Outcomes in 5 Cases of Pediatric and Adult Patients

Carlos Florez-Zorrilla1,2*, Karina Mendoza-Gallo2,3 and Josue Olivares-Del Moral1,2

1Hepatopancreatobiliary and Liver Transplant Surgery, Hospital Regional Valentín Gómez Farías-ISSSTE, Zapopan, México

2Hepatopancreatobiliary and Liver Transplant Surgery, Centro Médico Puerta de Hierro Andares, Zapópan, México

3Department of Pediatrics, Hospital General de Zona 89-IMSS, Guadalajara, México

*Corresponding Author: Carlos Florez-Zorrilla, Hepatopancreatobiliary and Liver Transplant Surgery, Hospital Regional Valentín Gómez Farías-ISSSTE, Zapopan, México.

Received: July 10, 2023; Published: August 23, 2023

Abstract

Undifferentiated embryonal sarcoma of the liver (UESL) is a very rare and uncommon liver malignancy from primary mesenchymal-derived cells. This malignancy is mostly diagnosed in the childhood and being exceptional in adults over 40 years. 5 cases of UESL were collected from 2016 to 2023, the patients were 9 to 65 years old and included 2 children and 3 adults. Tumor size ranged between 17 to 24 cm in diameter and predominantly showed fibrous pseudocapsule, mixoid matrix, spindle and polygonal cells and scarce eosinophilic cytoplasm. 4 patients underwent surgical resection and 1 was considered for chemotherapy. Although UESL has poor prognosis early diagnosis and complete tumor resection are the most important variables for long term survival.

 Keywords: Undifferentiated Embryonal Sarcoma; Liver; Hepatectomy; Pediatric; Adult

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Citation

Citation: Carlos Florez-Zorrilla., et al. “Undifferentiated Embryonal Sarcoma of the Liver. Clinical Features and Outcomes in 5 Cases of Pediatric and Adult Patients". Acta Scientific Gastrointestinal Disorders 6.9 (2023): 41-45.

Copyright

Copyright: © 2023 Carlos Florez-Zorrilla., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.




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