Niladri Das, Soumik Goswami, Arjun Baidya, Nilanjan Sengupta, Prashant Gaikwad, Deep Hathi and Silima S Tarenia*

Department of Endocrinology, Nilratan Sircar Medical College and Hospital, Kolkata, India

*Corresponding Author: Silima S Tarenia, Department of Endocrinology, Nilratan Sircar Medical College and Hospital, Kolkata, India.

Received: March 29, 2022; Published: April 20, 2022

Abstract

Pheochromocytoma is a catecholamine secreting adrenal tumor originating from chromaffin cells which accounts for 5% of ectopic ACTH syndrome cases and is infrequently reported in medical literature.

Case Description: A 36 year old woman presented with Cushingoid habitus, resistant hypertension, hypokalemia and recent onset diabetes. Endocrinological examination revealed ectopic ACTH production with hypercortisolemia and elevated plasma catecholamines. MRI abdomen showed a large left sided adrenal tumor. After initial medical management, left adrenalectomy resulted in complete remission of Cushing’s syndrome and pheochromocytoma.

Conclusion: We present here a case of ACTH producing pheochromocytoma with clinical features of Cushing syndrome.

Keywords: Pheochromocytoma; Ectopic ACTH Syndrome; Cushing’s Syndrome

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Citation: Niladri Das., et al. “Double Trouble: Cushing's Syndrome Due to ACTH-secreting Pheochromocytoma". Acta Scientific Clinical Case Reports 3.5 (2022): 72-75.

Copyright: © 2022 Niladri Das., et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.