Abstract

  Solid pseudopapillary tumor of pancreas is a very rare tumor of low malignant potential accounting for only 2 - 3% of all pancreatic neoplasms. It affects females of African American ethnicity. The tumor biology is unique in itself. It is seen that vascular invasion, degree of nuclear atypia, mitotic count and prominence of necrobiotic cell nests (cells with pycnotic nuclei and eosinophilic cytoplasm) are associated with malignancy. However, neoplasms in which above mentioned criteria of malignancy are not detected may also give rise to metastases. Hence benign appearing SPNs must be classified as lesions of uncertain malignant potential and must be operated on. Here we present a 27-year-old lady with 3 cm space occupying lesion in the head of the pancreas. Endoscopic ultrasonography guided biopsy revealed Solid Pseudopapillary Tumor of pancreas. Pancreaticoduodenectomy was carried out without significant complications and she was discharged on post-operative day 7. As this is a very rare tumor one encounters, we thought of reporting it.

Keywords: Pancreas; Solid Pseudopapillary Tumor of pancreas; Histology; Immunohistochemistry; Treatment; ancreaticoduodenectomy

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Citation

Citation: Gaurav Kumar., et al. “Encountering a Very Rare Pancreatic Tumor-Solid Pseudopapillary Tumor of Pancreas”. Acta Scientific Gastrointestinal Disorders 3.4 (2020): 15-19.

Copyright

Copyright: © 2020 Gaurav Kumar., et al.This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.